How are congenital cochlear malformations treated?

Congenital cochlear malformation is a disease caused by incomplete development of the inner part of the ear and is a common disease in daily life. The clinical manifestation of congenital cochlear malformation is usually incomplete hearing development or even no hearing at birth, so the impact on newborns is extremely severe. Therefore, parents must take a positive attitude to find ways to treat congenital cochlear malformations. So how should congenital cochlear malformations be treated?

1. Surgical treatment is mainly used to improve hearing. General anesthesia for young children. Anyone with normal inner ear function is suitable for surgery. Bilateral ear patients should undergo surgery early, preferably at 6 to 7 years old, and no younger than 4 years old. For patients with unilateral ear who have normal hearing in the other ear, surgery should be performed after adulthood. However, there is no age limit for patients with ear fistula or cholesteatoma accompanied by infection.

2. The surgical method and scope should be flexibly selected according to the characteristics of the deformity and the principles of tympanoplasty. For patients with well-developed auricle, the tympanic membrane may be intact and the external auditory canal route can be used. For patients with poorly developed auricle, the tympanic sinus route is safer. First, open the epitympanic cavity, carefully explore whether the ossicular chain and stapes are active, and then decide on the hearing reconstruction method. The reconstructed external auditory canal opening should be 1 times wider than normal. Cochlear implant

3. Deformed auricle should be treated according to plastic surgery principles. Congenital cochlear malformations can be divided into five types depending on their location and degree. The most serious of these is the underdevelopment of the entire inner ear, also known as "empty cochlea". Hearing aids are of no help to patients with this type of inner ear developmental abnormality. In addition, other types of inner ear developmental abnormalities, such as enlarged vestibular aqueduct and incomplete cochlear hypoplasia, can be compensated for by hearing aids. Some of the effects are very significant, and hearing and speech abilities are significantly improved after wearing them. Therefore, never give up on hearing aid fitting and hearing and language rehabilitation training for deaf children with inner ear developmental abnormalities.

The above is the treatment method for congenital cochlear malformations. I believe that parents and friends have already had a certain understanding. Although it is regrettable that it is congenital, it is not without treatment. Therefore, if a newborn baby is found to have congenital cochlear malformation, effective treatment must be taken as soon as possible.